技术文章

Recombinant Human Hamartin Protein: Research Guide

Recombinant Human Hamartin Protein is a recombinant form of the TSC1 gene product that serves as a critical tumor suppressor and negative regulator of the mTOR signaling pathway, enabling researchers to investigate its biochemical roles in cell growth, proliferation, and tuberous sclerosis complex disease mechanisms.

Gene Name
TSC1
Protein Common Name
Hamartin
Biological Function
Tumor suppressor; forms the TSC1-TSC2 (hamartin-tuberin) complex to negatively regulate mTORC1 signaling
Disease Relevance
Loss-of-function mutations in TSC1 are associated with Tuberous Sclerosis Complex (TSC), a rare autosomal dominant disorder
Product SKU
rp365374
Supplier Reference
absea#PP-937
Recommended Storage
Store at -80 °C for long-term; avoid repeated freeze-thaw cycles

Biological Background and Significance of Hamartin (TSC1)

Hamartin, encoded by the TSC1 gene located on chromosome 9q34, is a 130 kDa cytoplasmic scaffold protein that functions as a critical tumor suppressor. Its primary mechanism of action involves forming a stable heterodimeric complex with Tuberin (encoded by TSC2). Together, the TSC1-TSC2 complex acts as a GTPase-activating protein (GAP) toward the small GTPase Rheb, converting active Rheb-GTP to inactive Rheb-GDP, thereby suppressing the mechanistic target of rapamycin complex 1 (mTORC1) activity.

Dysregulation of this pathway leads to uncontrolled mTORC1 activation, driving excessive cell growth, proliferation, and survival — hallmarks of tumor formation. Loss-of-function mutations in either TSC1 or TSC2 are causally linked to Tuberous Sclerosis Complex (TSC), a rare autosomal dominant multisystem disorder characterized by benign hamartomas in the brain, kidneys, skin, lungs, and heart, with significant neurological morbidity including epilepsy and intellectual disability.

Beyond TSC, hamartin is implicated in broader cancer biology, autophagy regulation, and cellular energy sensing, making it a high-value research target across oncology, neurology, and cell biology disciplines.

Protein Characteristics and Product Specifications

Recombinant Human Hamartin Protein (SKU: rp365374; Supplier Ref: absea#PP-937) is produced using recombinant expression technology to provide researchers with a well-characterized, consistent source of TSC1 protein for in vitro biochemical and cell-based assays.

Key protein characteristics include:

  • Gene: TSC1
  • Species: Human (Homo sapiens)
  • Alternative Names: Hamartin, TSC1, Tuberous Sclerosis 1 Protein
  • Molecular Weight: The full-length human hamartin protein has a predicted molecular weight of approximately 130 kDa; the apparent molecular weight on SDS-PAGE may differ due to post-translational modifications and anomalous migration.
  • Formulation: Specific buffer composition and additives should be confirmed from the Certificate of Analysis (CoA) supplied with each lot.
  • Purity: Researchers should verify purity grade from the product CoA or by contacting Aladdin Scientific technical support.

Note: Detailed specifications including exact purity percentage, host expression system, tag information, and concentration are subject to lot-specific CoA. Please request the CoA for your specific lot prior to experimental use.

Research Applications

Recombinant Human Hamartin Protein supports a wide range of biochemical and cell biology research applications. Validated and suggested uses include:

  • Protein-protein interaction studies: Investigating the TSC1-TSC2 (hamartin-tuberin) complex formation, binding domains, and interaction with regulatory partners such as Rheb, FKBP38, and ERK.
  • mTOR pathway biochemical assays: Reconstitution of TSC complex GAP activity toward Rheb-GTP in cell-free systems to study upstream regulation of mTORC1.
  • Antibody validation: Use as a positive control antigen for Western blot, ELISA, and immunoprecipitation antibody validation experiments.
  • Structural biology: Supplying purified protein for crystallography, cryo-EM, or hydrogen-deuterium exchange mass spectrometry (HDX-MS) studies of hamartin domain architecture.
  • Drug discovery screening: Identification and validation of small-molecule modulators of TSC1 interactions or stability in biochemical binding assays.
  • Functional rescue experiments: In vitro complementation assays to study functional consequences of TSC1 mutations identified in TSC patients.

Note: Optimal working concentrations for each application should be determined empirically by the end user. Please consult the CoA and Aladdin Scientific technical support for application-specific guidance.

Quality Assurance and Regulatory Considerations

Aladdin Scientific is committed to supplying research-grade recombinant proteins that meet consistent quality standards. For Recombinant Human Hamartin Protein (rp365374), the following quality considerations apply:

  • Certificate of Analysis (CoA): Each lot is accompanied by a CoA detailing purity, concentration, biological activity (where applicable), endotoxin levels, and recommended storage conditions. Request the lot-specific CoA before use.
  • Endotoxin testing: For cell-based applications, ensure endotoxin levels are within acceptable limits as stated on the CoA. High endotoxin levels can confound cellular assays.
  • Research use only (RUO): This product is intended exclusively for research purposes and is NOT approved for diagnostic, therapeutic, or clinical use in humans or animals.
  • Lot-to-lot consistency: While Aladdin Scientific maintains rigorous production standards, researchers performing longitudinal studies are advised to reserve sufficient quantity from a single validated lot to ensure experimental consistency.
  • Safety: Handle according to standard laboratory biosafety practices. Consult the Safety Data Sheet (SDS) for complete hazard information and disposal guidelines.

Frequently asked questions

What is hamartin and why is it important for mTOR signaling research?

Hamartin (TSC1) is a tumor suppressor protein that heterodimerizes with tuberin (TSC2) to form the TSC1-TSC2 complex, which acts as a GAP toward Rheb GTPase and thereby suppresses mTORC1 activity. Loss-of-function mutations in TSC1 lead to constitutive mTORC1 activation, underlying Tuberous Sclerosis Complex disease and contributing to broader oncogenic signaling, making it a central target in mTOR pathway research.

How should I store Recombinant Human Hamartin Protein to maintain activity?

For long-term storage, aliquot the protein immediately upon receipt and store at -80 °C. For short-term use within one week, storage at 4 °C in the supplied buffer is acceptable. Avoid repeated freeze-thaw cycles, as they promote protein aggregation and activity loss. Always consult the lot-specific Certificate of Analysis for confirmed storage recommendations.

What in vitro applications is Recombinant Human Hamartin Protein suitable for?

Recombinant Human Hamartin Protein is suited for protein-protein interaction studies (e.g., TSC1-TSC2 complex assembly), biochemical GAP activity assays toward Rheb, antibody validation as a positive control antigen in Western blot and ELISA, structural biology studies, and small-molecule drug discovery screening. Optimal concentrations for each specific application should be determined empirically.

Is Recombinant Human Hamartin Protein suitable for clinical or diagnostic use?

No. Recombinant Human Hamartin Protein from Aladdin Scientific (rp365374) is strictly a Research Use Only (RUO) product. It is not approved, validated, or intended for use in clinical diagnostics, therapeutic applications, or any procedure involving human or animal patients.

How do I request a Certificate of Analysis (CoA) for my lot of rp365374?

You can request a lot-specific Certificate of Analysis by contacting Aladdin Scientific's customer service or technical support team with your order number and lot number. The CoA will provide confirmed purity, concentration, endotoxin levels, and storage conditions specific to your product lot.

References

  1. Inoki K, Li Y, Xu T, Guan KL. Rheb GTPase is a direct target of TSC2 GAP activity and regulates mTOR signaling. Genes Dev. 2003;17(15):1829-1834. doi:10.1101/gad.1110003
  2. van Slegtenhorst M, de Hoogt R, Hermans C, et al. Identification of the tuberous sclerosis gene TSC1 on chromosome 9q34. Science. 1997;277(5327):805-808. doi:10.1126/science.277.5327.805
  3. Huang J, Manning BD. The TSC1-TSC2 complex: a molecular switchboard controlling cell growth. Biochem J. 2008;412(2):179-190. doi:10.1042/BJ20080281

Products are supplied for research and development use only. Not for use in humans, animals, diagnosis, or therapy.

目录: 技术文章

Da — 若无特别说明,分子量单位默认为道尔顿。   Mw — 重均分子量。   Mn — 数均分子量。

产品仅供科研与开发使用,不用于人体、动物、诊断或治疗。

引用本文

阿拉丁科学.《Recombinant Human Hamartin Protein: Research Guide》. 阿拉丁知识库,更新于 2026年11月2日。 https://www.aladdin-e.com/zh_cn/faqs/recombinant-human-hamartin-protein-research-guide-en.html
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